hrp0095p2-234 | Pituitary, Neuroendocrinology and Puberty | ESPE2022

Management of precocious puberty in girls with McCune–Albright syndrome

Abdelaziz Foued , Selim Nihad , Khansal Sabrina , Bouchair Nadira

McCune-Albright syndrome is a rare, sporadic disorder defined by the triad of café-au-lait spots, fibrous bone dysplasia, and endocrinopathy. The diagnosis is often made on bone or endocrine involvement, but must be suspected on the particular morphology of café-au-lait spots. We report a case of McCune-Albright syndrome diagnosed on these cutaneous signs and precocious puberty. This is a 4.5-year-old girl referred by a gynecologist for a pediatric endocrinology ...